Abstract

ESTUPINAN-DIAZ, Bárbara O. et al. Meningioangiomatosis and focal cortical dysplasia. Rev Ecuat Neurol [online]. 2022, vol.31, n.2, pp.103-109. ISSN 2631-2581.  https://doi.org/10.46997/revecuatneurol31200103.

The association between meningioangiomatosis (MA) with focal cortical dysplasia (FCD) has been scarcely published. We present the case of 15-year-old adolescent suffering 10 years evolving drug-resistant epilepsy without history of neurofibromatosis. Magnetic Resonance Image showed an increase in the volume of the hippocampus and the right parahippocampal region. The lesion was considered as a possible tumor. A right temporal lobectomy, guided by trans-surgical electrocorticography (EcoG) was performed. Histology of the resected tissue evidenced a FCD type IIIc (MA mainly vascular associated to FCD). The patient has been seizure free (according to the Engel IA scale) after 4 years of post-surgical evolution. When MA is suspected, we recommend trans-surgical ECoG considering the possible association with FCD in the surrounding neocortex. It could increase the incidence and knowledge about these two lesions. The histological study provides the definitive diagnosis.

Keywords : Epilepsy surgery; Focal cortical dysplasia type IIIc; Drug resistant epilepsy; Malformations of cortical development; Sporadic meningioangiomatosis..

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