ESTUPINAN-DIAZ, Bárbara O. et al. Meningioangiomatosis and focal cortical dysplasia. []. , 31, 2, pp.103-109. ISSN 2631-2581.  https://doi.org/10.46997/revecuatneurol31200103.

The association between meningioangiomatosis (MA) with focal cortical dysplasia (FCD) has been scarcely published. We present the case of 15-year-old adolescent suffering 10 years evolving drug-resistant epilepsy without history of neurofibromatosis. Magnetic Resonance Image showed an increase in the volume of the hippocampus and the right parahippocampal region. The lesion was considered as a possible tumor. A right temporal lobectomy, guided by trans-surgical electrocorticography (EcoG) was performed. Histology of the resected tissue evidenced a FCD type IIIc (MA mainly vascular associated to FCD). The patient has been seizure free (according to the Engel IA scale) after 4 years of post-surgical evolution. When MA is suspected, we recommend trans-surgical ECoG considering the possible association with FCD in the surrounding neocortex. It could increase the incidence and knowledge about these two lesions. The histological study provides the definitive diagnosis.

: Epilepsy surgery; Focal cortical dysplasia type IIIc; Drug resistant epilepsy; Malformations of cortical development; Sporadic meningioangiomatosis..

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